Autoimmune pancreatitis (AIP) is a type of chronic pancreatitis characterized by an autoimmune manifestations revealed on imaging, laboratory, histologic, and clinical study. In the past 10 years, interest and reports of autoimmune pancreatitis has grown rapidly because of an increasing ability to diagnose it with growing awareness of the disease entity and the use of new markers of disease and pancreatic biopsy.1,2 Autoimmune pancreatitis is a rare systemic fibroinflammatory disease which can affect not only the pancreas, but also a variety of organs such as the bile ducts, salivary glands, retroperitoneum, and lymph nodes. Organs affected by AIP have a lymphoplasmacytic infiltrate rich in IgG4-positive cells. This inflammatory process responds dramatically to oral steroid therapy.
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